Recurrent Meningitis and Mondini Dysplasia

Laurie A. Ohlms, Morven S. Edwards, Edward Mason, Makoto Igarashi, Bobby R. Alford, Richard J.H. Smith

Research output: Contribution to journalArticlepeer-review

88 Scopus citations


Three infants with cerebrospinal fluid otorrhea and recurrent meningitis due to Mondini dysplasia have been treated at Baylor College of Medicine, Houston, Tex; 39 other patients with this association have been described. This review highlights the characteristics and embryologic basis of the malformation. The clinical evaluation of an infant with recurrent meningitis is outlined, and the importance of brain-stem response audiometry and thincut computed tomography of the temporal bones is discussed. Surgical management depends on the functional status of the dysplastic ear; usually, a stapedectomy is performed and the vestibule is obliterated. Although the surgical failure rate is 30% after one procedure, early identification of the dysplasia and prompt surgical management diminish morbidity and mortality and permit early habilitation of the child with congenital hearing impairment.

Original languageEnglish (US)
Pages (from-to)608-612
Number of pages5
JournalArchives of Otolaryngology--Head and Neck Surgery
Issue number5
StatePublished - May 1990

ASJC Scopus subject areas

  • Surgery
  • Otorhinolaryngology


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