TY - JOUR
T1 - Primitive myxoid mesenchymal tumor of infancy involving chest wall in an infant
T2 - A case report and clinicopathologic correlation
AU - Foster, Jennifer H.
AU - Vasudevan, Sanjeev A.
AU - Hicks, M. John
AU - Schady, Deborah
AU - Chintagumpala, Murali
PY - 2016/5/1
Y1 - 2016/5/1
N2 - Primitive myxoid mesenchymal tumor of infancy (PMMTI) is a rare mesenchymal tumor of early childhood characterized by aggressive local infiltration of surrounding structures, rare metastases, and poor response to chemotherapy. Surgery alone appears to be the most effective treatment given the lack of predilection for metastasis and poor response to traditional chemotherapy. Below we report a patient with PMMTI successfully managed with surgery and observation and summarize the existing literature on histopathologic features and treatment of this lesion.
AB - Primitive myxoid mesenchymal tumor of infancy (PMMTI) is a rare mesenchymal tumor of early childhood characterized by aggressive local infiltration of surrounding structures, rare metastases, and poor response to chemotherapy. Surgery alone appears to be the most effective treatment given the lack of predilection for metastasis and poor response to traditional chemotherapy. Below we report a patient with PMMTI successfully managed with surgery and observation and summarize the existing literature on histopathologic features and treatment of this lesion.
KW - Primitive myxoid mesenchymal tumor of infancy
KW - Rare tumors
KW - Sarcoma
UR - http://www.scopus.com/inward/record.url?scp=84977627834&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=84977627834&partnerID=8YFLogxK
U2 - 10.2350/15-05-1644-CR.1
DO - 10.2350/15-05-1644-CR.1
M3 - Article
C2 - 26516796
AN - SCOPUS:84977627834
SN - 1093-5266
VL - 19
SP - 244
EP - 248
JO - Pediatric and Developmental Pathology
JF - Pediatric and Developmental Pathology
IS - 3
ER -