Low-grade myofibroblastic sarcoma of the sacrum: Case report

William E. Humphries; Krishna B. Satyan; Katherine Relyea; Eugene S. Kim; Adekunle M. Adesina; Murali Chintagumpala; Andrew Jea

doi:10.3171/2010.5.PEDS09289

Low-grade myofibroblastic sarcoma of the sacrum: Case report

William E. Humphries, Krishna B. Satyan, Katherine Relyea, Eugene S. Kim, Adekunle M. Adesina, Murali Chintagumpala, Andrew Jea

Research output: Contribution to journal › Article

9 Scopus citations

Abstract

Myofibroblastic tumors are soft-tissue neoplasms arising from myofibroblasts, ubiquitous cells sharing ultrastructural features of muscular and fibroblastic cells. Vasudev and Harris described a malignant counterpart of these benign tumors in 1978. Most reported cases of myofibroblastic sarcoma have arisen in the head and neck region and the soft tissues of the extremities. To the best of the authors' knowledge, there have been only 8 previous reports on primary myofibroblastic sarcoma of the bone. The authors report a new case of this rare tumor affecting the sacrum and ilium of a 15-year-old girl and discuss the role of total sacrectomy and lumbopelvic reconstruction for treatment of this disease.

Original language	English (US)
Pages (from-to)	286-290
Number of pages	5
Journal	Journal of Neurosurgery: Pediatrics
Volume	6
Issue number	3
DOIs	https://doi.org/10.3171/2010.5.PEDS09289
State	Published - Sep 2010

Keywords

Myofibroblastic sarcoma
Pediatric spine
Sacrectomy

ASJC Scopus subject areas

Clinical Neurology
Surgery
Pediatrics, Perinatology, and Child Health

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title = "Low-grade myofibroblastic sarcoma of the sacrum: Case report",

abstract = "Myofibroblastic tumors are soft-tissue neoplasms arising from myofibroblasts, ubiquitous cells sharing ultrastructural features of muscular and fibroblastic cells. Vasudev and Harris described a malignant counterpart of these benign tumors in 1978. Most reported cases of myofibroblastic sarcoma have arisen in the head and neck region and the soft tissues of the extremities. To the best of the authors' knowledge, there have been only 8 previous reports on primary myofibroblastic sarcoma of the bone. The authors report a new case of this rare tumor affecting the sacrum and ilium of a 15-year-old girl and discuss the role of total sacrectomy and lumbopelvic reconstruction for treatment of this disease.",

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AU - Chintagumpala, Murali

AU - Jea, Andrew

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