Low-grade myofibroblastic sarcoma of the sacrum: Case report

William E. Humphries; Krishna B. Satyan; Katherine Relyea; Eugene S. Kim; Adekunle M. Adesina; Murali Chintagumpala; Andrew Jea

doi:10.3171/2010.5.PEDS09289

Low-grade myofibroblastic sarcoma of the sacrum: Case report

William E. Humphries, Krishna B. Satyan, Katherine Relyea, Eugene S. Kim, Adekunle M. Adesina, Murali Chintagumpala, Andrew Jea

Research output: Contribution to journal › Article › peer-review

9 Scopus citations

Abstract

Myofibroblastic tumors are soft-tissue neoplasms arising from myofibroblasts, ubiquitous cells sharing ultrastructural features of muscular and fibroblastic cells. Vasudev and Harris described a malignant counterpart of these benign tumors in 1978. Most reported cases of myofibroblastic sarcoma have arisen in the head and neck region and the soft tissues of the extremities. To the best of the authors' knowledge, there have been only 8 previous reports on primary myofibroblastic sarcoma of the bone. The authors report a new case of this rare tumor affecting the sacrum and ilium of a 15-year-old girl and discuss the role of total sacrectomy and lumbopelvic reconstruction for treatment of this disease.

Original language	English (US)
Pages (from-to)	286-290
Number of pages	5
Journal	Journal of Neurosurgery: Pediatrics
Volume	6
Issue number	3
DOIs	https://doi.org/10.3171/2010.5.PEDS09289
State	Published - Sep 2010

Keywords

Myofibroblastic sarcoma
Pediatric spine
Sacrectomy

ASJC Scopus subject areas

Clinical Neurology
Surgery
Pediatrics, Perinatology, and Child Health

Access to Document

10.3171/2010.5.PEDS09289

Fingerprint Dive into the research topics of 'Low-grade myofibroblastic sarcoma of the sacrum: Case report'. Together they form a unique fingerprint.

Cite this

@article{ddac2aff51cd4ac5a067ca049a8c69e2,

title = "Low-grade myofibroblastic sarcoma of the sacrum: Case report",

abstract = "Myofibroblastic tumors are soft-tissue neoplasms arising from myofibroblasts, ubiquitous cells sharing ultrastructural features of muscular and fibroblastic cells. Vasudev and Harris described a malignant counterpart of these benign tumors in 1978. Most reported cases of myofibroblastic sarcoma have arisen in the head and neck region and the soft tissues of the extremities. To the best of the authors' knowledge, there have been only 8 previous reports on primary myofibroblastic sarcoma of the bone. The authors report a new case of this rare tumor affecting the sacrum and ilium of a 15-year-old girl and discuss the role of total sacrectomy and lumbopelvic reconstruction for treatment of this disease.",

keywords = "Myofibroblastic sarcoma, Pediatric spine, Sacrectomy",

author = "Humphries, {William E.} and Satyan, {Krishna B.} and Katherine Relyea and Kim, {Eugene S.} and Adesina, {Adekunle M.} and Murali Chintagumpala and Andrew Jea",

year = "2010",

month = sep,

doi = "10.3171/2010.5.PEDS09289",

language = "English (US)",

volume = "6",

pages = "286--290",

journal = "Journal of Neurosurgery: Pediatrics",

issn = "1933-0707",

publisher = "American Association of Neurological Surgeons",

number = "3",

}

TY - JOUR

T1 - Low-grade myofibroblastic sarcoma of the sacrum

T2 - Case report

AU - Humphries, William E.

AU - Satyan, Krishna B.

AU - Relyea, Katherine

AU - Kim, Eugene S.

AU - Adesina, Adekunle M.

AU - Chintagumpala, Murali

AU - Jea, Andrew

PY - 2010/9

Y1 - 2010/9

N2 - Myofibroblastic tumors are soft-tissue neoplasms arising from myofibroblasts, ubiquitous cells sharing ultrastructural features of muscular and fibroblastic cells. Vasudev and Harris described a malignant counterpart of these benign tumors in 1978. Most reported cases of myofibroblastic sarcoma have arisen in the head and neck region and the soft tissues of the extremities. To the best of the authors' knowledge, there have been only 8 previous reports on primary myofibroblastic sarcoma of the bone. The authors report a new case of this rare tumor affecting the sacrum and ilium of a 15-year-old girl and discuss the role of total sacrectomy and lumbopelvic reconstruction for treatment of this disease.

AB - Myofibroblastic tumors are soft-tissue neoplasms arising from myofibroblasts, ubiquitous cells sharing ultrastructural features of muscular and fibroblastic cells. Vasudev and Harris described a malignant counterpart of these benign tumors in 1978. Most reported cases of myofibroblastic sarcoma have arisen in the head and neck region and the soft tissues of the extremities. To the best of the authors' knowledge, there have been only 8 previous reports on primary myofibroblastic sarcoma of the bone. The authors report a new case of this rare tumor affecting the sacrum and ilium of a 15-year-old girl and discuss the role of total sacrectomy and lumbopelvic reconstruction for treatment of this disease.

KW - Myofibroblastic sarcoma

KW - Pediatric spine

KW - Sacrectomy

UR - http://www.scopus.com/inward/record.url?scp=77956627450&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=77956627450&partnerID=8YFLogxK

U2 - 10.3171/2010.5.PEDS09289

DO - 10.3171/2010.5.PEDS09289

M3 - Article

C2 - 20809714

AN - SCOPUS:77956627450

VL - 6

SP - 286

EP - 290

JO - Journal of Neurosurgery: Pediatrics

JF - Journal of Neurosurgery: Pediatrics

SN - 1933-0707

IS - 3

ER -

Low-grade myofibroblastic sarcoma of the sacrum: Case report

Abstract

Keywords

ASJC Scopus subject areas

Access to Document

Other files and links

Cite this