TY - JOUR
T1 - Low-grade myofibroblastic sarcoma of the sacrum
T2 - Case report
AU - Humphries, William E.
AU - Satyan, Krishna B.
AU - Relyea, Katherine
AU - Kim, Eugene S.
AU - Adesina, Adekunle M.
AU - Chintagumpala, Murali
AU - Jea, Andrew
PY - 2010/9
Y1 - 2010/9
N2 - Myofibroblastic tumors are soft-tissue neoplasms arising from myofibroblasts, ubiquitous cells sharing ultrastructural features of muscular and fibroblastic cells. Vasudev and Harris described a malignant counterpart of these benign tumors in 1978. Most reported cases of myofibroblastic sarcoma have arisen in the head and neck region and the soft tissues of the extremities. To the best of the authors' knowledge, there have been only 8 previous reports on primary myofibroblastic sarcoma of the bone. The authors report a new case of this rare tumor affecting the sacrum and ilium of a 15-year-old girl and discuss the role of total sacrectomy and lumbopelvic reconstruction for treatment of this disease.
AB - Myofibroblastic tumors are soft-tissue neoplasms arising from myofibroblasts, ubiquitous cells sharing ultrastructural features of muscular and fibroblastic cells. Vasudev and Harris described a malignant counterpart of these benign tumors in 1978. Most reported cases of myofibroblastic sarcoma have arisen in the head and neck region and the soft tissues of the extremities. To the best of the authors' knowledge, there have been only 8 previous reports on primary myofibroblastic sarcoma of the bone. The authors report a new case of this rare tumor affecting the sacrum and ilium of a 15-year-old girl and discuss the role of total sacrectomy and lumbopelvic reconstruction for treatment of this disease.
KW - Myofibroblastic sarcoma
KW - Pediatric spine
KW - Sacrectomy
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U2 - 10.3171/2010.5.PEDS09289
DO - 10.3171/2010.5.PEDS09289
M3 - Article
C2 - 20809714
AN - SCOPUS:77956627450
SN - 1933-0707
VL - 6
SP - 286
EP - 290
JO - Journal of Neurosurgery: Pediatrics
JF - Journal of Neurosurgery: Pediatrics
IS - 3
ER -