We report two rare cases of biopsy proven Immunoglobulin G4-related sclerosing orbital inflammation (IgG4SOI). The first case had intracranial involvement which, to our knowledge, is the first IgG4SOI case with serum cerebrospinal fluid abnormalities and the second case had an unusual presentation of a compressive optic neuropathy and systemic lymphadenopathy.
- Compressive optic neuropathy
- Immunoglobulin G4-positive sclerosing idiopathic orbital inflammation
- Immunoglobulin G4-positive with intracranial involvement
- Sclerosing idiopathic orbital inflammation
- Systemic lymphadenopathy
ASJC Scopus subject areas
- Clinical Neurology