From A… to… Z(OOR): The Clinical Spectrum of Acute Zonal Occult Outer Retinopathy

Margaret Wang, Ama Sadaka, Thomas Prager, Andrew G. Lee, Francesco Pellegrini, Daniele Cirone, Luca De Simone, Luca Cimino

Research output: Contribution to journalArticlepeer-review

8 Scopus citations


Acute idiopathic blind spot enlargement (AIBSE) is often caused by Acute Zonal Occult Outer Retinopathy (AZOOR), an outer retinal disease. We report two illustrative cases of AZOOR. The first one was a 21-year-old white female who presented with a scotoma and “shimmering lights” in her left eye. In the second case, a 73-year-old white female was referred for evaluation of a “bitemporal hemianopsia” that started years prior, with no clinical significant photopsias. To our knowledge, case two is the longest documented duration of bilateral, progressive, and chronic, idiopathic, enlargement of the blind spot (CIBSE) documented in the English language ophthalmic literature.

Original languageEnglish (US)
Pages (from-to)215-221
Number of pages7
Issue number4
StatePublished - Jul 4 2018


  • Acute zonal occult outer retinopathy
  • autofluorescence
  • ellipsoid zone
  • enlarged blind spot

ASJC Scopus subject areas

  • Ophthalmology
  • Clinical Neurology


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