Dandy Walker malformation and hypertrophic cardiomyopathy: Unusual fatal association

Maher E. Kurdi, Mohammed A. Chamsi-Pasha, Saleh S. Baeesa, Mohammed M. Jan

Research output: Contribution to journalArticlepeer-review

2 Scopus citations


Dandy Walker malformation (DWM) is a rare congenital brain anomaly characterized by cystic dilation of the fourth ventricle and hypoplasia of the cerebellar vermis. Other extracranial anomalies can be associated, including cardiac defects. We report a rare patient with DWM associated with progressive heart failure secondary to hypertrophic cardiomyopathy. He was diagnosed at 2 months of age and died 5 months later. We conclude that hypertrophic cardiomyopathy can be associated with DWM with poor prognosis. A careful cardiac evaluation is needed in all infants with DWM for early recognition of such potentially serious associated cardiac malformations.

Original languageEnglish (US)
Pages (from-to)368-370
Number of pages3
Issue number4
StatePublished - Oct 1 2009

ASJC Scopus subject areas

  • Clinical Neurology
  • Psychiatry and Mental health


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