TY - JOUR
T1 - Basal cell nevus syndrome concurrent with adenoid cystic carcinoma of salivary gland
AU - Yilmaz, Belma
AU - Goldberg, Leonard H.
AU - Schechter, Naomi R.
AU - Kemp, Bonnie L.
AU - Ruiz, Hiram
PY - 2003/5/1
Y1 - 2003/5/1
N2 - Basal cell nevus syndrome is a genetically determined disease characterized by 5 major manifestations (multiple basal cell carcinomas, jaw cysts, skeletal abnormalities, pits of the hands and feet, and ectopic calcification) and a variety of developmental anomalies. We present a case of basal cell nevus syndrome in which the patient bad adenoid cystic carcinoma of the minor salivary glands develop in the soft palate resulting in distant pulmonary metastases. The patient died at the age of 44 years of respiratory complications. To our knowledge, this is the first simultaneous occurrence of basal cell nevus syndrome with adenoid cystic carcinoma of salivary gland.
AB - Basal cell nevus syndrome is a genetically determined disease characterized by 5 major manifestations (multiple basal cell carcinomas, jaw cysts, skeletal abnormalities, pits of the hands and feet, and ectopic calcification) and a variety of developmental anomalies. We present a case of basal cell nevus syndrome in which the patient bad adenoid cystic carcinoma of the minor salivary glands develop in the soft palate resulting in distant pulmonary metastases. The patient died at the age of 44 years of respiratory complications. To our knowledge, this is the first simultaneous occurrence of basal cell nevus syndrome with adenoid cystic carcinoma of salivary gland.
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U2 - 10.1067/mjd.2003.164
DO - 10.1067/mjd.2003.164
M3 - Article
C2 - 12734479
AN - SCOPUS:0038284764
SN - 0190-9622
VL - 48
SP - S64-S66
JO - Journal of the American Academy of Dermatology
JF - Journal of the American Academy of Dermatology
IS - 5 SUPPL.
ER -