Basal cell nevus syndrome concurrent with adenoid cystic carcinoma of salivary gland

Belma Yilmaz, Leonard Harry Goldberg, Naomi R. Schechter, Bonnie L. Kemp, Hiram Ruiz

Research output: Contribution to journalArticle

12 Scopus citations

Abstract

Basal cell nevus syndrome is a genetically determined disease characterized by 5 major manifestations (multiple basal cell carcinomas, jaw cysts, skeletal abnormalities, pits of the hands and feet, and ectopic calcification) and a variety of developmental anomalies. We present a case of basal cell nevus syndrome in which the patient bad adenoid cystic carcinoma of the minor salivary glands develop in the soft palate resulting in distant pulmonary metastases. The patient died at the age of 44 years of respiratory complications. To our knowledge, this is the first simultaneous occurrence of basal cell nevus syndrome with adenoid cystic carcinoma of salivary gland.

Original languageEnglish (US)
JournalJournal of the American Academy of Dermatology
Volume48
Issue number5 SUPPL.
DOIs
StatePublished - May 1 2003

ASJC Scopus subject areas

  • Dermatology

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